What the Anesthesiologist Should Know before the Operative Procedure Cystic fibrosis (CF) is an autosomal recessive multisystem disease caused by a mutation in the CF transmembrane conductance regulator gene on chromosome 7. Incidence is 1 in 3200 children and pulmonary disease accounts for 85% of mortality. Etiology of lung disease is obstruction of the airway…
What the Anesthesiologist Should Know before the Operative Procedure Cystic hygroma (CH) (i.e., cystic lymphangioma) is a congenital cystic tumor-like mass representing a malformation of lymphatic tissue. Incidence is 1 in 12,000 births in the United States and affects both sexes equally. Etiology is failure of peripheral lymphatic vessels to flow into the jugular sacs…
What the Anesthesiologist Should Know before the Operative Procedure Choledochal cysts (CCs) are rare medical conditions due to aberrant dilatation of the common bile duct that may cause obstruction in biliary flow. Incidence in western population is 1 in 100,000 to 150,000 live births, although the incidence is as high as 1 in 13,500 in…
What the Anesthesiologist Should Know before the Operative Procedure Congenital laryngeal cysts are rare in children with an incidence of 1/300,000 per live births (1.82 per 100,000 live births in certain populations) and are classified into ductal cysts, saccular cysts, and thyroid-cartilage foraminal cysts. The most common type, ductal cysts, may originate anywhere in the…
What the Anesthesiologist Should Know before the Operative Procedure Congenital cystic lesions of the neck include midline and lateral defects, in descending order of frequency, thyroglossal duct cyst, branchial cleft anomalies, dermoid cysts, hemangiomas, and lymphangiomas. Malformations of the midline Thyroglossal duct cysts (TDCs) are the most common congenital cyst encountered in the neck, representing…
What the Anesthesiologist Should Know before the Operative Procedure Congenital cystic adenomatoid malformation (CCAM) is a rare bronchopulmonary abnormality (incidence1/20,000-1/30,000 live births) that accounts for 95% of congenital cystic disease. Etiology is unknown but hypothesized to be due to embryologic insult resulting in cessation of bronchial maturation, absence of bronchial cartilage, and suppression of normal…
